Brain Arteriovenous Malformations (AVM’S)


What is an AVM?
Arteriovenous malformations, or AVM’s, are a collection of abnormal vessels which may occur within virtually any part of the brain tissue. Blood normally flows from the heart through arteries to supply all organs including the brain. Four major arteries supply the brain, two carotid arteries in the front of the neck and two vertebral arteries in the back of the neck.


Normally blood is pumped from the heart into the large arteries at relatively high pressure and speed which decreases as the blood flow reaches smaller and smaller arteries. Eventually the blood reaches the smallest vessels called capillaries. Capillaries are smaller than the diameter of a human hair and as the blood flows slowly through these tiny vessels, it gives up oxygen and nutrients to the brain tissue and receives carbon dioxide and other waste products. The blood then enters tiny veins at very low pressure, joining larger veins to return to the heart and lungs. Pressure and speed of blood flow in the veins are normally very low compared to that of the arteries. The walls of the veins are therefore relatively thin and delicate compared to those of the arteries.


AVM’s are abnormal communications or "short circuits" which directly connect relatively large arteries within the brain directly to veins. The blood is delivered at relatively higher pressure with more rapid flow directly into the veins. Because the veins were never designed to take the higher pressures and flows, they expand, pushing against the neighboring areas of normal brain. This may damage the normal brain causing weakness, numbness, loss of vision, or seizures. Often the supplying arteries, the AVM itself, or the enlarged veins rupture, resulting in the most common presentation of an AVM- intracranial hemorrhage, a type of stroke.


"Stroke" is a general term meaning interference with brain function caused by damage to the brain’s arteries or veins. Strokes may result from hemorrhage, as mentioned above, when a vessel breaks or ruptures allowing blood to escape, similar to a leak in a pipe. In hemorrhage, the escaping blood may damage the surrounding brain directly and the tear in the vessel may prevent brain supplied by that vessel from receiving its normal blood flow. Hemorrhage or hemorrhagic stroke is the type of stroke most often caused by AVM’s.


How does one get an AVM?
AVM’s are most often congential (present at birth or early in life and slowly develop over time) and usually no specific cause for the AVM can be identified. In the vast majority of cases, AVM’s are not inherited and other members of the family are not at increased risk for having an AVM.


How are AVM’s diagnosed?
AVM’s are usually diagnosed by medical imaging studies, which are often ordered after a patient develops symptoms. Symptoms of an AVM may include headache, weakness, numbness, visual problems, seizures, or most often, the abrupt onset of stroke.
The first imaging study in patients who are suspected to have an AVM is usually a CT (computed tomography) scan or MRI (magnetic resonance imaging). These studies are quite good at identifying an AVM and are relatively noninvasive, requiring only an injection of contrast material into a small vein during the study.


Further identification of the vessels involved in the AVM requires a test called an angiogram or arteriogram. Angiography is the only test currently available which provides sufficiently detailed information on which to plan and carry out therapy of most AVM’s.


What is an angiogram?
Angiography is a study of the brain blood vessels. It is performed by a physician experienced and trained in performing and interpreting blood vessel examinations of the brain, using X-rays to map the specific blood vessels involved in the AVM. A small tube or catheter is inserted into the femoral artery in the groin and maneuvered into the vessels in the neck supplying the brain. Material called contrast or "dye" which is visible on the X-ray is injected into the vessel and images are taken as the liquid flows through the AVM. The angiogram gives a detailed picture of the vessels involved and the flow through the AVM. Based on the information gained by the angiogram, treatment options can be determined for each patient.


How are AVM’s treated?
There are three major treatment methods that may be useful either alone or in combination to treat an AVM. The specific treatment for an individual is based on that patient’s history, symptoms, and anatomy of the AVM including its size, feeding arteries, draining veins, and location within the brain. Treatments include: endovascular embolization (closure of the AVM from within the blood vessels), open surgical removal of the AVM, radiosurgery, or a combination of techniques.


Open surgical treatment involves removing a portion of the skull so that surgical instruments can be inserted to remove the AVM. Surgical treatment is often performed after embolization has closed portions of the AVM. The combination of embolization followed by surgical resection is frequently safer than surgical resection alone in treating an AVM.


Radiosurgery is a technique which uses focused beams of radiation to treat AVM’s which are sufficiently small and located in appropriate areas of the brain. Despite the name, no opening of the skull is required; instead the radiation causes scarring in blood vessels of the AVM, thereby eliminating it. After treating the AVM with radiosurgery, a period of two to three years is required for the full effect of the treatment to be determined. In over 80% of cases where the AVM is sufficiently small, there is complete obliteration of the AVM.


What is embolization?
Embolization is an endovascular technique, (performed from within the blood vessels) to block vessels of the AVM. Embolization is performed using catheters and angiographic techniques similar to those discussed above. For the embolization procedure, a very tiny catheter is threaded from the groin directly into the AVM vessels within the brain. Under X-ray guidance, material is injected through the catheter to permanently block and close off the vessels of the AVM. Materials used might include particles, small platinum coils, and/or liquid embolic agents similar to glue.


Embolization of an AVM is usually performed before treatment by either surgery or radiosurgery. Embolization is often able to decrease the size of the AVM making the surgery or radiosurgery much safer than would otherwise be the case. However, certain AVM’s blood flow may be totally blocked by embolization techniques, and no further therapy may be required.


Who performs endovascular embolization procedures?
Endovascular treatment is a relatively new type of treatment requiring specialized training. Most physicians who perform endovascular embolization are neuroradiologists or neurosurgeons who have received several years of additional training in navigating inside the brain blood vessels to treat a variety of blood vessel disorders.


What do I need to know before having an embolization?
The patient should not eat or drink anything after midnight on the night before the procedure. This is very important in that any food in the stomach will make the patient nauseated during the procedure and may cause vomiting with severe consequences. Patients should take their normal medications the morning of the procedure with a small amount of water. Embolizations are performed either under sedation or under general anesthesia. Procedures frequently take 4 to 6 hours and the time necessary is often not predictable before the procedure begins.


After the procedure, the patient will need to remain still and avoid bending the hip where the puncture occurred for at least 6-8 hours. This means lying flat and is often the portion of the entire experience that is most uncomfortable. The period of rest is very important since it allows the small puncture hole in the artery to heal. The potential complications and risks of the procedure should be discussed with your doctor.


Patients usually remain in the hospital for about several days following an embolization procedure. The first night is usually spent in the neurological intensive care unit for close monitoring, this is followed by transfer to a regular hospital room for 24 hours before discharge. If surgery is to follow the embolization procedure, it may be performed on the day after embolization. Sometimes multiple embolization procedures are necessary in order to get the maximum closure of the AVM safely, these are usually scheduled several weeks to months apart.


Will all my symptoms be cured by treatment of the AVM?
Treatment of an AVM is directed toward preventing brain injury including that which might result from bleeding or rebleeding. No treatment currently exists which can repair damage already done to the brain by the AVM. This means for example, that seizures might continue after embolization or even complete removal of the AVM. Patients with neurological deficits resulting from AVM hemorrhage would likely still have the deficits after treatment of the AVM, although improvement may occur.


For more information go to: www.asitn.org



Figure 1: AP angiograms demonstrate a large arteriovenous malformation of the left parietal region. The film on the left demonstrates the feeding arteries from the middle cerebral artery system with a large draining vein medially to the sagittal sinus. The film on the right demonstrates several large feeding vessels from the posterior cerebral artery on the left side.

Figure 2: The AVM of the patient shown in Figure 1 after endovascular embolization using N-butyl-cyanoacryalate glue for part of the AVM. As can be seen, the AP angiogram on the carotid circulation (left) shows a greatly diminished arterial to venous shunt. As well, the film of the right demonstrates decreased filling from the posterior cerebral supply to the AVM.

Figure 3: AP angiograms following surgical resection of the large AVM of the patient shown in Figures 1 and 2. Preoperative embolization made the operation safer with a minimum of blood loss at the time of operation. As can be seen on the carotid injection (left film). there is no arterial to venous shunting. The vertebral injection (right film) shows no AV shunting. The patient made an excellent recovery from surgery with no neurologic deficits

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